Test Code LRBA Lipopolysaccharide-Responsive Beige-Like Anchor Protein (LRBA) Deficiency, Blood
Test Down Notes
LRBA is temporarily test down due to reagent issues.
Ordering Guidance
This flow cytometry test is complementary to genetic testing.
Shipping Instructions
Testing is performed Monday through Friday. Specimens not received by 4 p.m. (CST) on Friday may be cancelled.
Collect and package specimen as close to shipping time as possible. It is recommended that specimens arrive within 24 hours of collection.
Samples arriving on the weekend and observed holidays may be canceled.
Necessary Information
Ordering healthcare professional name and phone number are required.
Specimen Required
Container/Tube: Lavender top (EDTA)
Specimen Volume: 3 mL
Collection Instructions: Send whole blood specimen in original tube. Do not aliquot.
Useful For
Aiding in the diagnosis of lipopolysaccharide-responsive beige-like anchor protein (LRBA) deficiency
This test is not useful for identifying a carrier status for LRBA deficiency.
Genetics Test Information
The human lipopolysaccharide-responsive beige-like anchor protein (LRBA) gene is on chromosome 4.
Assessment of 109 patients with LRBA deficiency has shown 93 homozygous and 16 compound heterozygous alterations in the gene.
Alterations in the LRBA gene have been observed throughout the length of the gene and include the following main categories: Nonsense; missense; insertions, deletions, indels, and splice site alterations.
Reporting Name
LRBA Deficiency, BSpecimen Type
Whole Blood EDTASpecimen Minimum Volume
1 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Whole Blood EDTA | Ambient | 48 hours | PURPLE OR PINK TOP/EDTA |
Reject Due To
Gross hemolysis | Reject |
Gross lipemia | Reject |
Gross icterus | OK |
Reference Values
The appropriate reference values will be provided on the report.
Specimen Retention Time
4 daysPerforming Laboratory
Mayo Clinic Laboratories in RochesterCPT Code Information
86356 x 2
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
LRBA | LRBA Deficiency, B | In Process |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
608960 | %CD3+LRBA+ | In Process |
608964 | MFI CD3+LRBA+ | In Process |
608961 | %CD19+LRBA+ | In Process |
608965 | MFI CD19+LRBA+ | In Process |
608968 | LRBA Interpretation | 69052-9 |
Day(s) Performed
Monday through Friday