Test Code VWD8B von Willebrand Disease 2N (Subtype Normandy), Plasma
Additional Testing Requirements
VWAG / von Willebrand Factor Antigen, Plasma; VWACT / von Willebrand Factor Activity, Plasma; and F8A / Coagulation Factor VIII Activity Assay, Plasma are recommended to supplement results of this test.
Necessary Information
If performed at another laboratory, forward the results of the following tests with the specimen:
-von Willebrand factor antigen
-VWF activity (ristocetin cofactor, latex immunoassay etc)
-Factor VIII activity
These results aid in the interpretation of this test.
Specimen Required
Specimen Type: Platelet-poor plasma
Collection Container/Tube: Light-blue top (3.2% sodium citrate)
Submission Container/Tube: Plastic vial
Specimen Volume: 1 mL
Collection Instructions:
1. For complete instructions, see Coagulation Guidelines for Specimen Handling and Processing
2. Centrifuge, transfer all plasma into a vial, and centrifuge plasma again.
3. Aliquot plasma into a separate tube leaving 0.25 mL in the bottom of the centrifuged vial.
4. Freeze plasma immediately (no longer than 4 hours after collection) at -20° C or, ideally, less than or equal to -40° C.
Additional Information:
1. Double-centrifuged specimen is critical for accurate results as platelet contamination may cause spurious results.
2. Each coagulation assay requested should have its own vial.
Forms
If not ordering electronically, complete, print, and send a Coagulation Test Request (T753) with the specimen.
Useful For
Diagnosing von Willebrand disease (VWD) type 2N
Evaluating patients diagnosed with mild-to-moderate hemophilia A with an autosomal inheritance pattern
Evaluating hemophilia A patients with a shortened survival of infused factor VIII (FVIII) (not caused by a specific FVIII inhibitor)
Evaluating female patients with low FVIII activity and no prior family history of hemophilia A
Evaluating patients with Type 1 or Types 2A, 2B, or 2M VWD with FVIII activity discordantly lower than the von Willebrand factor antigen level
Special Instructions
Reporting Name
VWD 2N (Normandy), PSpecimen Type
Plasma Na CitSpecimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Plasma Na Cit | Frozen | 56 days |
Reject Due To
Gross hemolysis | OK |
Gross lipemia | OK |
Gross icterus | OK |
Reference Values
68-106%
Pediatric reference ranges have not been established for this assay but likely achieve adult reference range by 18 years of age.
Day(s) Performed
Monthly on the third Thursday
Report Available
1 to 31 daysSpecimen Retention Time
7 daysPerforming Laboratory
Mayo Clinic Laboratories in RochesterCPT Code Information
85246
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
VWD8B | VWD 2N (Normandy), P | 90919-2 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
607336 | VWF:FVIIIB | 90919-2 |
607337 | VWF:FVIIIB Interpretation | 48595-3 |