Test Code PUPYU Purines and Pyrimidines Panel, Random, Urine
Useful For
Evaluating patients with symptoms suspicious for disorders of purine and pyrimidine metabolism
Monitoring patients with disorders of purine and pyrimidine metabolism
Laboratory evaluation of primary and secondary hyperuricemias
Disease States
- Lesch-Nyhan syndrome
- Secondary hyperuricemia
- Molybdenum cofactor deficiency
Reporting Name
Purines and Pyrimidines Panel, USpecimen Type
UrineOrdering Guidance
This is recommended screening test for the initial workup of a suspected disorder of purine and pyrimidine metabolism, particularly when clinical features are nonspecific, and includes measurement of purines, pyrimidines, uric acid, and S-sulfocysteine. If the clinical features are suggestive of molybdenum cofactor deficiency, isolated sulfite oxidase deficiency, and hereditary xanthinuria, order SSCTU / S-Sulfocysteine Panel, Urine.
If this test is ordered with SSCTU, then SSCTU will be canceled.
Necessary Information
Patient's age is required.
Specimen Required
Supplies: Urine Tubes, 10 mL (T068)
Container/Tube: Plastic, 10-mL urine tube
Specimen Volume: 3 mL
Collection Instructions: Collect a random urine specimen.
Specimen Minimum Volume
2 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Frozen | 90 days |
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Reference Values
Age range |
0-3 years |
4-6 years |
7-12 years |
13-18 years |
>18 years |
Uracil |
≤50 |
≤30 |
≤25 |
≤20 |
≤20 |
Thymine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Adenine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Hypoxanthine |
≤65 |
≤30 |
≤30 |
≤30 |
≤30 |
Xanthine |
≤54 |
≤21 |
≤35 |
≤15 |
≤20 |
Orotic |
≤4 |
≤4 |
≤3 |
≤3 |
≤5 |
Dihydroorotic acid |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Uric Acid |
350-2500 |
200-2000 |
200-1400 |
150-700 |
70-700 |
Deoxythymidine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Deoxyuridine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Thymidine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Uridine |
≤10 |
≤3 |
≤3 |
≤3 |
≤3 |
Deoxyadenosine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Deoxyinosine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Deoxyguanosine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Adenosine |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Inosine |
≤6 |
≤3 |
≤3 |
≤3 |
≤3 |
Guanosine |
≤4 |
≤3 |
≤3 |
≤3 |
≤3 |
5-Aminoimidazole-4-carboxamide 1-beta-D-ribofuranoside (AICAR) |
≤3 |
≤3 |
≤3 |
≤3 |
≤3 |
Succinyladenosine |
≤16 |
≤3 |
≤3 |
≤3 |
≤3 |
S-Sulfocysteine |
≤11 |
≤5 |
≤5 |
≤5 |
≤5 |
Dihydrouracil |
≤15 |
≤6 |
≤6 |
≤6 |
≤6 |
Dihydrothymine |
≤11 |
≤3 |
≤3 |
≤3 |
≤3 |
N-Carbamoyl-B-alanine |
≤30 |
≤10 |
≤10 |
≤10 |
≤10 |
N-Carbamoyl-B-aminoisobutyric |
≤20 |
≤3 |
≤3 |
≤3 |
≤3 |
All results reported as mmol/mol creatinine
Day(s) Performed
Tuesday, Thursday
Report Available
3 to 7 daysSpecimen Retention Time
1 monthPerforming Laboratory
Mayo Clinic Laboratories in RochesterCPT Code Information
82542
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
PUPYU | Purines and Pyrimidines Panel, U | 79673-0 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
42201 | Interpretation (PUPYU) | 79677-1 |
41978 | Uracil | 25140-5 |
38249 | Thymine | 48157-2 |
38239 | Adenine | 59203-0 |
41980 | Hypoxanthine | 38366-1 |
41981 | Xanthine | 38371-1 |
38246 | Orotic Acid | 17869-9 |
38251 | Dihydroorotic | 78694-7 |
41979 | Uric Acid | 34385-5 |
38252 | Deoxythymidine | 59215-4 |
38253 | Deoxyuridine | 59193-3 |
38248 | Thymidine | 59215-4 |
38250 | Uridine | 59216-2 |
38241 | Deoxyadenosine | 59199-0 |
38243 | Deoxyinosine | 59202-2 |
38242 | Deoxyguanosine | 59201-4 |
38240 | Adenosine | 75160-2 |
38245 | Inosine | 59210-5 |
38244 | Guanosine | 78691-3 |
38254 | AICAR | 75151-1 |
38247 | Succinyladenosine | 59214-7 |
606745 | S-Sulfocysteine | 33876-4 |
38255 | Dihydrouracil | 79685-4 |
38256 | Dihydrothymine | 78693-9 |
38257 | N-carbamoyl-beta-alanine | 59251-9 |
38258 | N-carbamoyl-beta-aminoisobutyric Acid | 79647-4 |
42200 | Reviewed By | 18771-6 |
Forms
If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.
Genetics Test Information
There are at least 35 known inherited disorders of purine and pyrimidine metabolism which cause a variety of neurological, immunological, hematological, and renal manifestations.