Test Code LAB1231958 Porphyrins, Quantitative, Random, Urine
Performing Laboratory
Mayo Clinic Laboratories in RochesterReporting Name
Porphyrins, QN, Random, USpecimen Type
UrineOrdering Guidance
This random urine test should be ordered when the specimen will reach Mayo Clinic Laboratories within 72 hours. If transportation will take longer than 72 hours, order PQNU / Porphyrins, Quantitative, 24 Hour, Urine and follow collection guidelines.
Shipping Instructions
Ship specimen in amber bottle to protect from light.
Necessary Information
Include a list of medications the patient is currently taking.
Specimen Required
Patient Preparation: Patient should not consume any alcohol for the 24 hours before specimen collection.
Supplies: Urine Container - Amber, 60 mL (T596)
Container/Tube: Amber, 60-mL urine container
Specimen Volume: 20 to 50 mL
Collection Instructions: Collect a random urine specimen.
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Frozen | 72 hours | LIGHT PROTECTED |
Specimen Minimum Volume
15 mL
Special Instructions
Day(s) Performed
Monday through Friday
Specimen Retention Time
1 weekReport Available
2 to 4 daysReference Values
Uroporphyrins, Octacarboxyl:
≤30 nmol/L
Heptacarboxylporphyrins:
≤7 nmol/L
Hexacarboxylporphyrins:
≤2 nmol/L
Pentacarboxyporphyrins:
≤5 nmol/L
Copropprphyrin, Tetracboxyl:
≤110 nmol/L
Porphobilinogen:
≤1.3 mcmol/L
Useful For
Preferred test to begin assessment for congenital erythropoietic porphyria and porphyria cutanea tarda and during symptomatic periods for acute intermittent porphyria, hereditary coproporphyria, and variegate porphyria when specimen transport will not exceed 72 hours
Testing Algorithm
The following algorithms are available:
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CPT Code Information
84110-Porphobilinogen, quantitative
84120-Porphyrins, quantitation and fractionation
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
PQNRU | Porphyrins, QN, Random, U | 93707-8 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
32332 | Uroporphyrin, Octa | 25166-0 |
32333 | Heptacarboxylporphyrins | 34314-5 |
32334 | Hexacarboxylporphyrins | 96795-0 |
32335 | Pentacarboxylporphyrins | 34352-5 |
32336 | Coproporphyrin, Tetra | 25167-8 |
32337 | Porphobilinogen | 2811-8 |
32338 | Interpretation | 49291-8 |
Disease States
- Porphyria
Genetics Test Information
This test is preferred test during symptomatic periods for acute intermittent porphyria, hereditary coproporphyria, and variegate porphyria. The random urine collection for this test allows for the diagnosis to be established and treatment to be initiated quickly. However, this test should only be ordered when the specimen will be received at Mayo Clinic Laboratories within 72 hours of collection. If it will be longer, PQNU / Porphyrins, Quantitative, 24 Hour, Urine should be ordered and collection guidelines must be followed.
Testing includes porphobilinogen which is useful in the evaluation of the acute porphyrias.
This is the preferred test to begin assessment for congenital erythropoietic porphyria and porphyria cutanea tarda.
Forms
If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.