Test Code LAB1059 Organic Acids Screen, Random, Urine
Performing Laboratory
Mayo Clinic Laboratories in Rochester
Reporting Name
Organic Acids Scrn, USpecimen Type
UrineNecessary Information
1. Patient's age is required.
2. Biochemical Genetics Patient Information (T602) is recommended, but not required, to be filled out and sent with the specimen to aid in the interpretation of test results.
Specimen Required
Supplies: Urine Tubes, 10 mL (T068)
Collection Container/Tube: Clean, plastic urine collection container
Submission Container/Tube: Plastic, 10-mL urine tube
Specimen Volume: 10 mL
Pediatric: If insufficient collection volume, submit as much specimen as possible in a single container; the laboratory will determine if volume is sufficient for testing.
Collection Instructions:
1. Collect a random urine specimen.
2. No preservative.
Reject Due To
All specimens will be evaluated at Mayo Clinic Laboratories for test suitability.Specimen Stability Information
| Specimen Type | Temperature | Time |
|---|---|---|
| Urine | Frozen (preferred) | 416 days |
| Refrigerated | 14 days |
Specimen Minimum Volume
4 mL
Special Instructions
Day(s) Performed
Monday through Saturday
Specimen Retention Time
2 monthsReport Available
3 to 5 daysReference Values
An interpretive report will be provided.
Useful For
Diagnosis of inborn errors of metabolism
Testing Algorithm
For information see Epilepsy: Unexplained Refractory and/or Familial Testing Algorithm
CPT Code Information
83919
LOINC Code Information
| Test ID | Test Order Name | Order LOINC Value |
|---|---|---|
| OAU | Organic Acids Scrn, U | 49287-6 |
| Result ID | Test Result Name | Result LOINC Value |
|---|---|---|
| 80619 | Organic Acids Scrn, U | 49287-6 |
Method Description
A urine volume corresponding to 0.25 mg of creatinine is acidified and then extracted with ethyl acetate. After separation and evaporation of the solvent phase, the dry residue is sialylated and analyzed by capillary gas chromatography mass spectrometry. When indicated, oxidation of 2-keto acids is performed by reaction with hydroxylamine hydrate.(Sweetman L. Organic acid analysis. In: Hommes FA, ed. Techniques in Diagnostic Human Biochemical Genetics. Wiley-Liss; 1991:143-176; Hoffman GF, Feyh P. Organic acid analysis. In: Blau N, Duran M, Blaskovics ME, Gibson KM, eds. Physician's Guide to the Laboratory Diagnosis of Metabolic Diseases. Springer; 2003:27-44; Cowan T, Pasquali M. Laboratory investigations of inborn errors of metabolism. In: Sarafoglou K, Hoffman GF, Roth KS, eds. Pediatric Endocrinology and Inborn Errors of Metabolism. 2nd ed. McGraw-Hill; 2017:1143)
Disease States
- Alkaptonuria
Forms
1. Biochemical Genetics Patient Information (T602)
2. If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.